Hemophilia B acquired after cadaveric liver transplantation: a case report.

Autor: Machado E Silva Gomide L; Department of Gastrointestinal Surgery and Liver Transplantation, Clinical Hospital of the Federal University of Paraná, Curitiba, PR, Brasil., Weihermann V; Department of General Surgery, Clinical Hospital of the Federal University of Paraná, Curitiba, PR, Brasil., de Oliveira IC; Department of General Surgery, Clinical Hospital of the Federal University of Paraná, Curitiba, PR, Brasil., Nissel MAZ; Department of General Surgery, Clinical Hospital of the Federal University of Paraná, Curitiba, PR, Brasil., Valejo IRM; Department of General Surgery, Clinical Hospital of the Federal University of Paraná, Curitiba, PR, Brasil., da Silva Wolff L; Department of General Surgery, Clinical Hospital of the Federal University of Paraná, Curitiba, PR, Brasil., de Aguiar AJ; Department of Gastrointestinal Surgery and Liver Transplantation, Clinical Hospital of the Federal University of Paraná, Curitiba, PR, Brasil., Verona D; Department of General Surgery, Clinical Hospital of the Federal University of Paraná, Curitiba, PR, Brasil., Degraf Y; Department of General Surgery, Clinical Hospital of the Federal University of Paraná, Curitiba, PR, Brasil., de Carvalho Arouca JS; Department of General Surgery, Clinical Hospital of the Federal University of Paraná, Curitiba, PR, Brasil., Barros Sanches JP; Department of General Surgery, Clinical Hospital of the Federal University of Paraná, Curitiba, PR, Brasil., Cabral RRS; Department of General Surgery, Clinical Hospital of the Federal University of Paraná, Curitiba, PR, Brasil., Kampa KC; Department of Gastrointestinal Surgery and Liver Transplantation, Clinical Hospital of the Federal University of Paraná, Curitiba, PR, Brasil., de Freitas ACT; Department of Gastrointestinal Surgery and Liver Transplantation, Clinical Hospital of the Federal University of Paraná, Curitiba, PR, Brasil.; Department of General Surgery, Clinical Hospital of the Federal University of Paraná, Curitiba, PR, Brasil., Tefili NL; Department of Gastrointestinal Surgery and Liver Transplantation, São Vicente Hospital, Curitiba, PR, Brasil.
Jazyk: angličtina
Zdroj: Journal of surgical case reports [J Surg Case Rep] 2022 Sep 05; Vol. 2022 (9), pp. rjac393. Date of Electronic Publication: 2022 Sep 05 (Print Publication: 2022).
DOI: 10.1093/jscr/rjac393
Abstrakt: Hemophilia B is a recessive hereditary disease, and manifestations result from coagulation factor IX deficiency. Although improbable, as factor IX is produced exclusively in the liver, the possibility of developing the disease after transplantation represents an infrequent but potentially morbid complication. Standard laboratory tests may be insufficient to determine the probability of transmission of this pathology. This report describes the case of a patient who developed hemophilia B after liver transplantation whose donor had no prior knowledge of the disease.
(Published by Oxford University Press and JSCR Publishing Ltd. © The Author(s) 2022.)
Databáze: MEDLINE
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