Embryonal Rhabdomyosarcoma of the Biliary Tree as a Differential in a Paediatric Patient Presenting with Biliary Dilatation: Not Always a Choledochal Cyst.

Autor:	Tripathy TP; Department of Radiodiagnosis, AIIMS, Bhubaneswar, India., Patidar Y; Department of Interventional Radiology, Institute of Liver & Biliary Sciences.; D-1 Vasant Kunj, New Delhi-110070, India., Chandel K; Department of Intervention Radiology, Institute of Liver & Biliary Sciences.; D-1 Vasant Kunj, New Delhi-110070, India., Varadarajan A; Department of pathology, Institute of Liver & Biliary Sciences.; D-1 Vasant Kunj, New Delhi-110070, India., Sood V; Department of Pediatric hepatology, Institute of Liver & Biliary Sciences.; D-1 Vasant Kunj, New Delhi-110070, India., Laroia ST; Department of Radiology, Institute of Liver & Biliary Sciences.; D-1 Vasant Kunj, New Delhi-110070, India.
Jazyk:	angličtina
Zdroj:	Acta medica Lituanica [Acta Med Litu] 2022; Vol. 29 (1), pp. 112-117. Date of Electronic Publication: 2022 Jan 24.
DOI:	10.15388/Amed.2021.29.1.2
Abstrakt:	Rhabdomyosarcoma is a soft tissue malignant musculoskeletal tumour and is the most prevalent soft-tissue sarcoma in the paediatric population. Although, Embryonal RMS of the biliary tree is a rare entity, however, it is the most common cause of paediatric malignant obstructive jaundice. We present a 4-year-old child who had symptoms of obstructive jaundice and palpable liver. The non-contrast magnetic resonance imaging and magnetic resonance cholangiopancreatography (MRCP) features were consistent with choledochal cyst. However, contrast enhanced computed tomography and PET CT images revealed biliary RMS as the differential diagnosis. Percutaneous biopsy followed by histopathology confirmed the diagnosis of embryonal biliary RMS. Since embryonal rhabdomyosarcoma is uncommonly recorded in the literature and can mimic the appearance of a choledochal cyst, this case report emphasises the necessity of keeping embryonal RMS as a differential in paediatric cases of obstructive jaundice. (Copyright © 2022 Tara Prasad Tripathy, Yashwant Patidar, Karamvir Chandel, Annapoorani Varadarajan, Vikrant Sood, Shalini Thapar Laroia. Published by Vilnius University Press.)
Databáze:	MEDLINE
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