Case report: Restrictive cardiomyopathy presenting with complete thromboembolism occlusion of the terminal part of the abdominal aorta in a preadolescent Saudi girl.
Autor: | Al-Shammari AA; Department of Pediatrics, College of Medicine, Imam Abdulrahman Bin Faisal University, Dammam, Saudi Arabia.; King Fahd Hospital of the University, Khobar, Saudi Arabia., Muslim RA; College of Medicine, Imam Abdulrahman Bin Faisal University, Dammam, Saudi Arabia., Almuslim J; College of Medicine, Imam Abdulrahman Bin Faisal University, Dammam, Saudi Arabia., Elashaal E; King Fahd Hospital of the University, Khobar, Saudi Arabia.; Department of Surgery, College of Medicine, Imam Abdulrahman Bin Faisal University, Dammam, Saudi Arabia., Lardhi H; King Fahd Hospital of the University, Khobar, Saudi Arabia.; Department of Surgery, College of Medicine, Imam Abdulrahman Bin Faisal University, Dammam, Saudi Arabia., AlQahtani SA; Department of Pediatrics, College of Medicine, Imam Abdulrahman Bin Faisal University, Dammam, Saudi Arabia.; King Fahd Hospital of the University, Khobar, Saudi Arabia., AlBassam BN; Department of Pediatrics, College of Medicine, Imam Abdulrahman Bin Faisal University, Dammam, Saudi Arabia.; King Fahd Hospital of the University, Khobar, Saudi Arabia., Lardhi A; Department of Pediatrics, College of Medicine, Imam Abdulrahman Bin Faisal University, Dammam, Saudi Arabia.; King Fahd Hospital of the University, Khobar, Saudi Arabia. |
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Jazyk: | angličtina |
Zdroj: | Frontiers in pediatrics [Front Pediatr] 2022 Jul 19; Vol. 10, pp. 944627. Date of Electronic Publication: 2022 Jul 19 (Print Publication: 2022). |
DOI: | 10.3389/fped.2022.944627 |
Abstrakt: | Restrictive cardiomyopathy (RCM) is a rare disease in children, accounting for <5% of all pediatric cardiomyopathies. It may be idiopathic or may be a secondary to a systemic disease. The disease is characterized by normal systolic function with impaired ventricular filling caused by stiff ventricular walls. Children with RCM often present with symptoms of exercise intolerance, shortness of breath, weakness, and chest discomfort. Thromboembolism events are an unusual presentation of RCM. We are reporting a preadolescent female from the eastern province of Saudi Arabia who presented with sudden right lower limb swelling, paresthesia, and pain caused by a complete occlusion of the terminal part of the abdominal aorta and both common iliac arteries. Echocardiography revealed dilated atria, normal ventricle dimensions and two floating thrombi in the left atrium. The patient was successfully managed with an anticoagulant, surgical thrombectomy and cardiac transplantation. (Copyright © 2022 Al-Shammari, Muslim, Almuslim, Elashaal, Lardhi, AlQahtani, AlBassam and Lardhi.) |
Databáze: | MEDLINE |
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