[Ebstein's anomaly with ventricular preexcitation in an adult patient].

Autor: Inzunza-Cervantes G; Instituto Mexicano del Seguro Social, Centro Médico Nacional del Noroeste, Hospital de Especialidades No. 2 'Luis Donaldo Colosio Murrieta', Servicio de Cardiología. Ciudad Obregón, Sonora, México., Herrera-Gavilanes JR; Instituto Mexicano del Seguro Social, Centro Médico Nacional del Noroeste, Hospital de Especialidades No. 2 'Luis Donaldo Colosio Murrieta', Servicio de Cardiología. Ciudad Obregón, Sonora, México., Espinoza-Escobar G; Instituto Mexicano del Seguro Social, Centro Médico Nacional del Noroeste, Hospital de Especialidades No. 2 'Luis Donaldo Colosio Murrieta', Servicio de Cardiología. Ciudad Obregón, Sonora, México., Zazueta-Armenta V; Instituto Mexicano del Seguro Social, Centro Médico Nacional del Noroeste, Hospital de Especialidades No. 2 'Luis Donaldo Colosio Murrieta', Servicio de Cardiología. Ciudad Obregón, Sonora, México., Cortés-García VA; Instituto Mexicano del Seguro Social, Centro Médico Nacional del Noroeste, Hospital de Especialidades No. 2 'Luis Donaldo Colosio Murrieta', Servicio de Cardiología. Ciudad Obregón, Sonora, México., Ornelas-Aguirre JM; Universidad de Sonora, Departamento de Ciencias de la Salud. Ciudad Obregón, Sonora, México.
Jazyk: Spanish; Castilian
Zdroj: Revista medica del Instituto Mexicano del Seguro Social [Rev Med Inst Mex Seguro Soc] 2022 Jul 04; Vol. 60 (4), pp. 466-473. Date of Electronic Publication: 2022 Jul 04.
Abstrakt: Background: Ebstein's anomaly is a rare complex congenital heart disease, first described in 1866 by physician Wilhelm Ebstein, characterized by anatomical and functional malformations of the tricuspid valve and the right ventricle because of inadequate delaminization of the tricuspid valve tissue. By presenting a clinical case and reviewing the literature, we analyzed the approach of an adult patient with Ebstein anomaly with ventricular preexcitation.
Clinical Case: We describe the case of a 34-year-old male patient, with a clinical history of palpitations and dyspnea, and his paraclinics documented Ebstein type B anomaly associated with patent foramen oval and paroxysmal supraventricular tachycardia, Successful radiofrequency ablation was performed and tricuspid valvuloplasty was proposed.
Conclusion: It is concluded that Ebstein's anomaly is complex with clinical, morphological and physiopathological heterogeneous spectrum. Manifested from severe symptomatic forms in the neonatal period to asymptomatic or minimally symptomatic ones detected incidentally. Its diagnosis is based on clinical suspicion and confirmed by echocardiography or imaging studies. The therapeutic strategy may be based on medical management in its mild asymptomatic forms up to surgical interventions that include tricuspid valvuloplasty, palliative surgery, valve replacement or cardiac transplantation.
(© 2022 Revista Medica del Instituto Mexicano del Seguro Social.)
Databáze: MEDLINE
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