Hyperostosis in orbital rhabdomyosarcoma.

Autor:	Rogelio PNA; Department of Ophthalmology and Visual Sciences, Philippine General Hospital, Manila, Philippines pnarogeliomd@gmail.com., Ranche FKT; Department of Ophthalmology and Visual Sciences, Philippine General Hospital, Manila, Philippines., Pe-Yan MR; Department of Ophthalmology and Visual Sciences, Philippine General Hospital, Manila, Philippines.
Jazyk:	angličtina
Zdroj:	BMJ case reports [BMJ Case Rep] 2022 Jun 20; Vol. 15 (6). Date of Electronic Publication: 2022 Jun 20.
DOI:	10.1136/bcr-2021-245466
Abstrakt:	Rhabdomyosarcoma is the most common soft-tissue sarcoma in paediatric patients and may arise as a primary orbital neoplasm. Imaging studies show a unilateral solitary orbital lesion. With larger tumours, erosion of the adjacent orbital walls is a common accompanying bony change. We present an unusual case of rhabdomyosarcoma in a preschool girl with proptosis and temporal bossing. Imaging studies showed a homogeneous, well-delineated, extraconal mass of the right orbit with hyperostosis of the adjacent sphenoid bone. After excision of the mass and debulking of the sphenoid bone, histopathology showed embryonal rhabdomyosarcoma with no malignant infiltration of the adjacent bone. This is the first reported case of hyperostosis associated with rhabdomyosarcoma. Periosteal reaction is the proposed underlying mechanism. Competing Interests: Competing interests: None declared. (© BMJ Publishing Group Limited 2022. No commercial re-use. See rights and permissions. Published by BMJ.)
Databáze:	MEDLINE
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