Spontaneous Near Fatal Hemorrhage into Neurofibromatosis Type 1 Lesion in the Scalp.
| Autor: | Stephen E; Vascular Surgery Unit, Department of Surgery, Sultan Qaboos University Hospital, Muscat, Oman., Kariyattil R; Neurosurgery Unit, Department of Surgery, Sultan Qaboos University Hospital, Muscat, Oman., Mittal A; Department of Radiology, Sultan Qaboos University Hospital, Muscat, Oman., Al-Azri F; Department of Radiology, Sultan Qaboos University Hospital, Muscat, Oman., Al-Wahaibi K; Vascular Surgery Unit, Department of Surgery, Sultan Qaboos University Hospital, Muscat, Oman. |
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| Jazyk: | angličtina |
| Zdroj: | Oman medical journal [Oman Med J] 2022 May 31; Vol. 37 (3), pp. e387. Date of Electronic Publication: 2022 May 31 (Print Publication: 2022). |
| DOI: | 10.5001/omj.2022.02 |
| Abstrakt: | Neurofibromatosis type 1 (NF1) (von Recklinghausen's disease) is an autosomal dominant disorder characterized by café-au-lait spots, pigmented hamartomas of the iris, and multiple neurofibromas. Patients can present with hemorrhage secondary to trauma or rarely with spontaneous hemorrhage, both of which can be lethal and life-threatening. We report a 14-year-old girl with a rapidly expanding hematoma in a rare presentation of spontaneous bleed into the NF1 lesion in her scalp. Soon after presentation, she went into hemorrhagic shock. Emergency coiling of the left maxillary artery and branches successfully arrested the bleeding, while resuscitation reversed the hemorrhagic shock. (The OMJ is Published Bimonthly and Copyrighted 2022 by the OMSB.) |
| Databáze: | MEDLINE |
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