Inferior sinus venosus defect and anomalous hepatic venous return to the coronary sinus leading to an Eisenmenger syndrome.

Autor: Tajouri A; Marie-Lannelongue Hospital, Paediatric and Congenital Cardiac Surgery Department, Centre de Référence des Malformations Cardiaques Congénitales Complexes M3C Groupe Hospitalier Saint-Joseph, Paris-Saclay University, Plessis-Robinson, France., Batteux C; Marie-Lannelongue Hospital, Paediatric and Congenital Cardiac Surgery Department, Centre de Référence des Malformations Cardiaques Congénitales Complexes M3C Groupe Hospitalier Saint-Joseph, Paris-Saclay University, Plessis-Robinson, France.; UMRS 999, INSERM, Marie-Lannelongue Hospital, Paris-Saclay University, Le Plessis Robinson, France., Ly R; Hôpital Européen Georges Pompidou, adult congenital Cardiology Unit, Centre de Référence des Malformations Cardiaques Congénitales Complexes M3C, Paris, France., Houyel L; Hôpital Necker-Enfants Malades, Congenital and Pediatric Cardiology Unit, Centre de Référence des Malformations Cardiaques Congénitales Complexes M3C, Paris, France. Université de Paris, Paris, France., Hascoet S; Marie-Lannelongue Hospital, Paediatric and Congenital Cardiac Surgery Department, Centre de Référence des Malformations Cardiaques Congénitales Complexes M3C Groupe Hospitalier Saint-Joseph, Paris-Saclay University, Plessis-Robinson, France.; UMRS 999, INSERM, Marie-Lannelongue Hospital, Paris-Saclay University, Le Plessis Robinson, France.
Jazyk: angličtina
Zdroj: Cardiology in the young [Cardiol Young] 2022 Apr 28, pp. 1-2. Date of Electronic Publication: 2022 Apr 28.
DOI: 10.1017/S1047951122001354
Abstrakt: Inferior sinus venosus defect associated with left hepatic vein drainage to the coronary sinus is an extremely rare condition. We report the case of a 41-year-old man suffering from pulmonary arterial hypertension related to this unusual CHD. Planning of heart-lung transplantation in this case required accurate anatomical description.
Databáze: MEDLINE
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