IgG4-Related Disease Presenting as Hypertrophic Pachymeningitis.

Autor: Sapkota B; Rheumatology/Internal Medicine, University of Arkansas for Medical Sciences, Little Rock, USA., Rampure R; Rheumatology, University of Arkansas for Medical Sciences, Little Rock, USA., Gokden M; Pathology, University of Arkansas for Medical Sciences, Little Rock, USA., Kanuru S; Rheumatology, University of Arkansas for Medical Sciences, Little Rock, USA.
Jazyk: angličtina
Zdroj: Cureus [Cureus] 2022 Feb 02; Vol. 14 (2), pp. e21850. Date of Electronic Publication: 2022 Feb 02 (Print Publication: 2022).
DOI: 10.7759/cureus.21850
Abstrakt: IgG4-related disease (IgG4-RD) is a multi-organ, immune-mediated inflammatory condition of unknown etiology characterized by infiltration of tissues by IgG4 producing plasma cells. IgG4-related disease (IgG4-RD) can ideally affect any organs, but the involvement of the central nervous system (CNS) is a rare entity. We present a case of a 67-year-old male who presented with diplopia with imaging showing hypertrophic pachymeningitis (HPM) and was diagnosed with IgG4-RD of the CNS based on histopathology report.
Competing Interests: The authors have declared that no competing interests exist.
(Copyright © 2022, Sapkota et al.)
Databáze: MEDLINE