Cystic fibrosis in the 21st century: what every radiologist should know.

Autor: Hallouch O; Faculty of Medicine - Department of Radiology, Radiation Oncology and Nuclear Medicine, Université de Montréal, Montreal, Quebec, Canada., Marinos J; Faculty of Medicine - Department of Radiology, Radiation Oncology and Nuclear Medicine, Université de Montréal, Montreal, Quebec, Canada., Thibault F; Faculty of Medicine - Department of Radiology, Radiation Oncology and Nuclear Medicine, Université de Montréal, Montreal, Quebec, Canada., Vu KN; Faculty of Medicine - Department of Radiology, Radiation Oncology and Nuclear Medicine, Université de Montréal, Montreal, Quebec, Canada., Chalaoui J; Faculty of Medicine - Department of Radiology, Radiation Oncology and Nuclear Medicine, Université de Montréal, Montreal, Quebec, Canada., Bourgouin P; Faculty of Medicine - Department of Radiology, Radiation Oncology and Nuclear Medicine, Université de Montréal, Montreal, Quebec, Canada., Péloquin L; Faculty of Medicine - Department of Radiology, Radiation Oncology and Nuclear Medicine, Université de Montréal, Montreal, Quebec, Canada., Freire V; Faculty of Medicine - Department of Radiology, Radiation Oncology and Nuclear Medicine, Université de Montréal, Montreal, Quebec, Canada., Tremblay F; Faculty of Medicine - Department of Medicine, Université de Montréal, Montreal, Quebec, Canada., Chartrand-Lefebvre C; Faculty of Medicine - Department of Radiology, Radiation Oncology and Nuclear Medicine, Université de Montréal, Montreal, Quebec, Canada. Electronic address: carl.chartrand-lefebvre@umontreal.ca.
Jazyk: angličtina
Zdroj: Clinical imaging [Clin Imaging] 2022 Apr; Vol. 84, pp. 118-129. Date of Electronic Publication: 2022 Feb 12.
DOI: 10.1016/j.clinimag.2022.02.004
Abstrakt: Cystic Fibrosis (CF) is the most common lethal genetic disorder in Caucasian populations, affecting roughly 70,000 individuals worldwide. This autosomal recessive disorder causes a wide spectrum of multisystemic manifestations, most of which are either directly or indirectly related to defective epithelial chloride secretion. The current median life expectancy is 44 years; however, a significant proportion of the CF population now live into the 5th decade and beyond due to advances in treatment. As life expectancy of CF patients increases, there is a newly emerging adult CF population with unique radiological manifestations spanning multiple organ systems, which often require follow-up imaging. The goal of this article is to review the multiple systemic manifestations and complications of CF on different imaging modalities and explore the appropriate radiological follow up recommended.
(Copyright © 2022 Elsevier Inc. All rights reserved.)
Databáze: MEDLINE
Externí odkaz: