Snake Technique in Osler's Disease-Associated Thoracoabdominal Aortic Aneurysm.

Autor: Bessho S; Department of Thoracic and Cardiovascular Surgery, Mie University Hospital, Tsu, Japan., Ito H; Department of Thoracic and Cardiovascular Surgery, Mie University Hospital, Tsu, Japan. Electronic address: hisato.ito@gmail.com., Nakamura B; Department of Thoracic and Cardiovascular Surgery, Mie University Hospital, Tsu, Japan., Shomura Y; Department of Thoracic and Cardiovascular Surgery, Mie University Hospital, Tsu, Japan., Ogihara Y; Department of Cardiology and Nephrology, Mie University Hospital, Tsu, Japan., Yamada N; Department of Cardiology, Kuwana City Medical Center, Kuwana, Japan., Takao M; Department of Thoracic and Cardiovascular Surgery, Mie University Hospital, Tsu, Japan.
Jazyk: angličtina
Zdroj: The Annals of thoracic surgery [Ann Thorac Surg] 2022 Oct; Vol. 114 (4), pp. e283-e285. Date of Electronic Publication: 2022 Jan 05.
DOI: 10.1016/j.athoracsur.2021.12.010
Abstrakt: Osler's disease is an autosomal dominant disorder characterized by epistaxis, telangiectases, and arteriovenous malformations of the internal organs. Herein, we report the first published case of dissecting thoracoabdominal aortic aneurysm repair in a 66-year-old woman with hereditary hemorrhagic telangiectasia associated with ACVRL1 gene mutations. We maintained the activated clotting time around 400 seconds during cardiopulmonary bypass to avoid lethal hemorrhage from telangiectases or arteriovenous malformations. The Adamkiewicz artery could not be identified on imaging studies preoperatively. Therefore, we used the snake technique for intercostal revascularization, which was effective in preventing paraplegia.
(Copyright © 2022 The Society of Thoracic Surgeons. Published by Elsevier Inc. All rights reserved.)
Databáze: MEDLINE