| Autor: |
Dorney SF, Hassall EG, Arbuckle SM, Vargas JH, Berquist WE |
| Jazyk: |
angličtina |
| Zdroj: |
Australian paediatric journal [Aust Paediatr J] 1987 Feb; Vol. 23 (1), pp. 55-6. |
| DOI: |
10.1111/j.1440-1754.1987.tb02177.x |
| Abstrakt: |
A child is reported whose alpha-1-antitrypsin phenotype is SZ and who has chronic cholestatic liver disease that began in the neonatal period. Liver biopsy demonstrated paucity of the interlobular bile ducts, marked hepatocellular deposition in periportal areas of PAS-positive, diastase-resistant granules, and bridging portal fibrosis. The association of paucity of the interlobular bile ducts with SZ phenotype alpha-1-antitrypsin deficiency has not been reported previously. |
| Databáze: |
MEDLINE |
| Externí odkaz: |
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