Autor: |
Shamsaldeen Faden M; 1Department of Anesthesia and Critical Care, King Abdul-Aziz University Hospital, Jeddah, Kingdom Saudi Arabia;. Openheart32@gmail.com., Ahmed Noaman N; 1Department of Anesthesia and Critical Care, King Abdul-Aziz University Hospital, Jeddah, Kingdom Saudi Arabia;. Openheart32@gmail.com., Osman Osama OO; Department of Surgery, Cardiac Surgery Unit, King Abdul-Aziz University, Jeddah, Saudi Arabia. Openheart32@gmail.com., Elassal AA; Cardiothoracic Surgery Department, Zagazig University, Zagazig, Egypt. Openheart32@gmail.com., Al-Ghamdi AM; Cardiac Surgery Unit, Co-ordination Unit, King Abdul-Aziz University, Jeddah, Saudi Arabia. Openheart32@gmail.com., Debis R; 1Department of Anesthesia and Critical Care, King Abdul-Aziz University Hospital, Jeddah, Kingdom Saudi Arabia;. openheart32@gmail.com. |
Abstrakt: |
Ascending thoracic aortic aneurysms are rare in childhood and typically are seen in the setting of connective tissue defect syndromes. These aneurysms may lead to rupture, dissection, or valvular insufficiency, so root replacement is recommended. Here, we present a 17-month-old girl who presented with fever, cough, and pericardial effusion. Initially, we suspected this could be a COVID-19 case, so a nasopharyngeal swap was performed. An ascending aorta aneurysm involving the aortic arch was confirmed by echo, and urgent ascending aorta and arch replacement were done by utilizing the descending aorta as a new arch. The final diagnosis came with cutis laxa syndrome. In similar cases, good outcomes can be achieved with accurate diagnosis and appropriate surgical management. |