A Classic Presentation of Desmoplastic Small Round Cell Tumor.
| Autor: | Matute G; Pathology, Clinica Medellín, Medellín, COL., Franco Mira JA; Pathology, University of Cartagena, Cartagena, COL., Arroyave Toro A; Radiology, Health and Life Imaging, Medellín, COL., Quintero FA; Gynecologic Oncology, Colombian Cancer Foundation - Vida Clinic, Medellín, COL., Bernal JA; Surgical Oncology, Colombian Cancer Foundation - Vida Clinic, Medellín, COL., Solórzano F; Surgical Oncology, Colombian Cancer Foundation - Vida Clinic, Medellín, COL., Llinás Quintero N; Oncology, Colombian Cancer Foundation - Vida Clinic, Medellín, COL. |
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| Jazyk: | angličtina |
| Zdroj: | Cureus [Cureus] 2021 Aug 30; Vol. 13 (8), pp. e17582. Date of Electronic Publication: 2021 Aug 30 (Print Publication: 2021). |
| DOI: | 10.7759/cureus.17582 |
| Abstrakt: | Desmoplastic small round cell tumor (DSRCT) is a rare malignancy, of uncertain differentiation, which more commonly affects adolescents and young adult males; it usually has an intra-abdominal location. We describe the case of a 35-year-old male who presented initially with occasional abdominal pain, and subsequently with abdominal mass sensation, without any other associated symptoms. Imaging studies reported an intra-abdominal mass located in mesogastrium, right hypochondrium, and right lumbar region, without clear evidence of infiltration to secondary structures, but with clear peritoneal spread to greater omentum and pelvis. Definitive diagnosis of DSRCT is based on histologic and immunohistochemical findings. Standard treatment includes intensive neoadjuvant chemotherapy, surgical cytoreduction, and radiotherapy. Despite this multidisciplinary approach, DSRCT has a poor prognosis and a high mortality rate at five years. Competing Interests: The authors have declared that no competing interests exist. (Copyright © 2021, Matute et al.) |
| Databáze: | MEDLINE |
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