A rare case report of malignant peripheral nerve sheath tumor involving both the small bowel and large bowel.

Autor: Khan N; Department of Gastroenterology, St. Michael's Medical Center, Newark, NJ, an Affiliate of New York Medical College, Westchester, NY, USA., Hashmi I; Department of Internal Medicine, St. Michael's Medical Center, Newark, NJ, an Affiliate of New York Medical College, Westchester, NY, USA., Atallah L; Department of Internal Medicine, St. Michael's Medical Center, Newark, NJ, an Affiliate of New York Medical College, Westchester, NY, USA., Shaaban H; Department of Medical Oncology, St. Michael's Medical Center, Newark, NJ, an Affiliate of New York Medical College, Westchester, NY, USA., Guron G; Department of Medical Oncology, St. Michael's Medical Center, Newark, NJ, an Affiliate of New York Medical College, Westchester, NY, USA., Fedida A; Department of Gastroenterology, St. Michael's Medical Center, Newark, NJ, an Affiliate of New York Medical College, Westchester, NY, USA.
Jazyk: angličtina
Zdroj: Annals of African medicine [Ann Afr Med] 2021 Jul-Sep; Vol. 20 (3), pp. 228-231.
DOI: 10.4103/aam.aam_10_20
Abstrakt: Malignant peripheral nerve sheath tumor (MPNST) contains properties and histologic markers of both neural crest cells and mesenchymal cells. It is a rare diagnosis, with an incidence of 1:100,000/year or 4%-10% of soft-tissue sarcomas. There are very few cases reported and studied. Therefore, establishing a proper diagnosis and treatment of MPNST provides a challenge. We present this unique and rare case of metastatic MPNST of the small and large bowel with bone, pulmonary, liver, and splenic metastases. The patient subsequently developed hemorrhagic brain metastases and died 6 months after THE initial diagnosis.
Competing Interests: None
Databáze: MEDLINE
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