A child with Ewing's sarcoma in scapula: A rare case report.

Autor: Shashaa MN; Faculty of Medicine, University of Aleppo, Aleppo, Syria., Hamza A; Faculty of Medicine, University of Aleppo, Aleppo, Syria. Electronic address: Amr.f.hamza97@gmail.com., AlHashemi M; Faculty of Medicine, University of Aleppo, Aleppo, Syria., Alyousfi R; Department of Pathology, Aleppo University Hospital, University of Aleppo, Aleppo, Syria., Deebo MAA; Department of Orthopedic Surgery, Aleppo University Hospital, University of Aleppo, Aleppo, Syria., Katnaji J; Department of Orthopedic Surgery, Aleppo University Hospital, University of Aleppo, Aleppo, Syria.
Jazyk: angličtina
Zdroj: International journal of surgery case reports [Int J Surg Case Rep] 2021 Aug; Vol. 85, pp. 106182. Date of Electronic Publication: 2021 Jul 07.
DOI: 10.1016/j.ijscr.2021.106182
Abstrakt: Introduction: Ewing's sarcoma is considered to be the second most frequent primary sarcoma in children. It affects children and young adults with a male predominance. Ewing's sarcoma is usually found in the femur, humerus, ilium and tibia; and in extremely rare cases Ewing's sarcoma might affect the scapula. There are only 15 papers in PubMed database regarding scapular Ewing's sarcoma.
Case Presentation: A 14-year-old male, with no significant medical or surgical history, presented with a swelling in the right scapular area for two months. The patient also experienced mild pain and fever. On physical examination, there was a tender mass and restriction in the right shoulder joint movements. MRI showed a large scapular mass with the characteristics of a sarcoma. The final diagnosis was made based on pathologic findings. Eventually, the patient was subjected to neoadjuvant chemotherapy.
Discussion: The most common tumors affecting scapula are chondrosarcoma and osteosarcoma. In a cohort study about patients diagnosed with ES between 1988 and 2018, only 29 cases were involved in the scapula. There are 12 cases of congenital ES have been reported in the medical literature, 3 of them were in the shoulder girdle. Surgery with neoadjuvant chemotherapy is considered better for total survival in ES of scapula in comparison with chemotherapy and/or radiotherapy alone.
Conclusion: Ewing sarcoma is extremely rare in the scapula and should be considered as a differential diagnosis for any patient with scapular tumor.
(Copyright © 2021 The Authors. Published by Elsevier Ltd.. All rights reserved.)
Databáze: MEDLINE