A Rare Case of Dorsal Agenesis of Pancreas, Choledochal Cyst, and Hirschsprung Disease in a Young Patient.

Autor: Chapa UK; Division of GI and HPB Surgery Department of Surgery, Jawaharlal Institute of Postgraduate Medical Education and Research, Puducherry, India., Dutta S; Division of GI and HPB Surgery Department of Surgery, Jawaharlal Institute of Postgraduate Medical Education and Research, Puducherry, India., Remesh AM; Division of GI and HPB Surgery Department of Surgery, Jawaharlal Institute of Postgraduate Medical Education and Research, Puducherry, India., Jain A; Division of GI and HPB Surgery Department of Surgery, Jawaharlal Institute of Postgraduate Medical Education and Research, Puducherry, India., Abhinaya R; Division of GI and HPB Surgery Department of Surgery, Jawaharlal Institute of Postgraduate Medical Education and Research, Puducherry, India., Nelamangala Ramakrishnaiah VP; Division of GI and HPB Surgery Department of Surgery, Jawaharlal Institute of Postgraduate Medical Education and Research, Puducherry, India.
Jazyk: angličtina
Zdroj: ACG case reports journal [ACG Case Rep J] 2021 Apr 26; Vol. 8 (4), pp. e00561. Date of Electronic Publication: 2021 Apr 26 (Print Publication: 2021).
DOI: 10.14309/crj.0000000000000561
Abstrakt: Dorsal pancreatic agenesis is a rare congenital pancreatic malformation. There is just 1 reported case associating it with choledochal cyst. However, no cases have reported yet with both coexisting with Hirschsprung disease. We report a case of a 23-year-old man, presenting with on and off epigastric pain, sometimes radiating to the back. His medical records showed he had Hirschsprung disease as a neonate, for which he underwent Duhamel procedure. Ultrasound imaging revealed a choledochal cyst and a nonvisualized distal portion of the pancreas. Further cross-sectional imaging confirmed the findings-a type 1 choledochal cyst and a dorsal agenesis of the pancreas in a patient with Hirschsprung disease.
(© 2021 The Author(s). Published by Wolters Kluwer Health, Inc. on behalf of The American College of Gastroenterology.)
Databáze: MEDLINE
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