Cardiac lipoblastoma of the pulmonary valve: A rare tumor in an unusual location.

Autor: Feng T; Department of Cardiac Surgery, Beijing Children's Hospital affiliated to Capital Medical University, National Center for Children's Health, Beijing, China., Zhangke G; Department of Cardiac Surgery, Beijing Children's Hospital affiliated to Capital Medical University, National Center for Children's Health, Beijing, China., Song B; Department of Cardiac Surgery, Beijing Children's Hospital affiliated to Capital Medical University, National Center for Children's Health, Beijing, China.
Jazyk: angličtina
Zdroj: Journal of cardiac surgery [J Card Surg] 2021 Jul; Vol. 36 (7), pp. 2589-2591. Date of Electronic Publication: 2021 Apr 24.
DOI: 10.1111/jocs.15580
Abstrakt: Backgroud: Lipoblastoma is a rare, benign, fatty tissue tumour tumor that occurs in infancy and early childhood. Intrathoracic and mediastinal involvement of this tumour is rare, and an intracardiac location is even rarer.
Aims: To report the first case of a lipoblastoma in the pulmonary valve.
Materials: In this study, we report the case of a 15-month-old girl who presented with a tumour in the pulmonary valve.
Results: The tumour was completely resected macroscopically. Histological examination of the lesion confirmed the diagnosis of lipoblastoma.
Discussion: Most primary cardiac tumours are benign in the sense they are not invasive. However, benign tumours maintain the potential for serious illness related to significant haemodynamic compromise or life-threatening dysrhythmias. Due to the association of lipoblastoma with other heart malformations, preoperative diagnosis remains challenging.
Conclusion: Tumours on the heart valve are more likely to cause haemodynamic disturbances. Complete resection yields an excellent prognosis.
(© 2021 Wiley Periodicals LLC.)
Databáze: MEDLINE
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