Combined pulmonary fibrosis and emphysema in alpha-1-antitrypsin deficiency.

Autor: Le Beller A; Hospices Civils de Lyon, Department of Respiratory Medicine, National Coordinating Reference Center for Rare Pulmonary Diseases, Louis Pradel hospital, Lyon, France., Nasser M; Hospices Civils de Lyon, Department of Respiratory Medicine, National Coordinating Reference Center for Rare Pulmonary Diseases, Louis Pradel hospital, Lyon, France., Traclet J; Hospices Civils de Lyon, Department of Respiratory Medicine, National Coordinating Reference Center for Rare Pulmonary Diseases, Louis Pradel hospital, Lyon, France., Blanchet-Legens AS; Saint-Joseph Hospital, Department of respiratory medicine, Lyon, France., Kannengiesser C; Bichat Hospital, department of genetics; Paris Descartes University, Paris, France., Mornex JF; Hospices Civils de Lyon, Department of Respiratory Medicine, National Coordinating Reference Center for Rare Pulmonary Diseases, Louis Pradel hospital, Lyon, France; Claude-Bernard Lyon 1 University, University of Lyon, INRAE, IVPC, Lyon, France., Cottin V; Hospices Civils de Lyon, Department of Respiratory Medicine, National Coordinating Reference Center for Rare Pulmonary Diseases, Louis Pradel hospital, Lyon, France; Claude-Bernard Lyon 1 University, University of Lyon, INRAE, IVPC, Lyon, France. Electronic address: vincent.cottin@chu-lyon.fr.
Jazyk: angličtina
Zdroj: Respiratory medicine and research [Respir Med Res] 2021 May; Vol. 79, pp. 100819. Date of Electronic Publication: 2021 Mar 26.
DOI: 10.1016/j.resmer.2021.100819
Databáze: MEDLINE