Limited Scleroderma-Induced Pulmonary Arterial Hypertension Resulting in Impaired Postoperative Respiratory Function.

Autor: Shah FA; Internal Medicine, Lewis Gale Medical Center, Salem, USA., Mahler N; Internal Medicine, Lewis Gale Medical Center, Salem, USA., Braford M; Internal Medicine, Edward Via College of Osteopathic Medicine, Blacksburg, USA., Greene N; Pulmonary and Critical Care, Lewis Gale Medical Center, Salem, USA.
Jazyk: angličtina
Zdroj: Cureus [Cureus] 2021 Mar 06; Vol. 13 (3), pp. e13742. Date of Electronic Publication: 2021 Mar 06.
DOI: 10.7759/cureus.13742
Abstrakt: Limited scleroderma falls under the umbrella of systemic sclerosis, an autoimmune disease that presents with multiorgan dysfunction that includes pulmonary arterial hypertension. We examine a case of pulmonary arterial hypertension in an elderly nonsmoker with a history of limited scleroderma.  The patient presented with abdominal tenderness and was diagnosed with a sigmoid colonic stricture. She underwent laparoscopic bowel resection. During and after her surgery, she suffered from worsening respiratory function and decompensated, developing a large pleural effusion that led to a thoracentesis and a prolonged hospital course. Patients with scleroderma can develop acute symptoms involving several organ systems, including the colonic tract and lungs, as seen in our patient. A thorough workup and continuous close management and monitoring are necessary to avoid further complications in these patients, especially in the postoperative period.
Competing Interests: The authors have declared that no competing interests exist.
(Copyright © 2021, Shah et al.)
Databáze: MEDLINE