Iliopsoas Hematomas in a Patient with Progressive Encephalomyelitis with Rigidity and Myoclonus.

Autor: Shimazaki R; Department of Neurology, Tokyo Metropolitan Neurological Hospital, Japan., Mukai M; Department of Neurology, Tokyo Metropolitan Neurological Hospital, Japan., Nagaoka U; Department of Neurology, Tokyo Metropolitan Neurological Hospital, Japan., Sugaya K; Department of Neurology, Tokyo Metropolitan Neurological Hospital, Japan., Takahashi K; Department of Neurology, Tokyo Metropolitan Neurological Hospital, Japan.
Jazyk: angličtina
Zdroj: Internal medicine (Tokyo, Japan) [Intern Med] 2021 Aug 01; Vol. 60 (15), pp. 2475-2477. Date of Electronic Publication: 2021 Feb 15.
DOI: 10.2169/internalmedicine.6604-20
Abstrakt: Progressive encephalomyelitis with rigidity and myoclonus (PERM) is a rare and severe syndrome characterized by rigidity of the limb and truncal muscles, brainstem signs, myoclonus, and hyperekplexia. Iliopsoas hematoma is a serious complication of bleeding disorders that occurs most commonly in patients with hemophilia and also in association with anti-coagulant drug treatment. We herein present a case of PERM complicated with bilateral iliopsoas hematomas. His neurological symptoms improved after immunotherapy, and thereafter the iliopsoas hematomas disappeared. Neurologists should consider iliopsoas hematomas as a serious potential complication of PERM.
Databáze: MEDLINE