Amniotic band syndrome with double encephalocele: A case report.

Autor: da Silva AJF; Department of Pediatric Neurosurgery, Santa Monica Maternity School - Alagoas State University of Health Sciences, Maceio, Alagoas, Brazil., Silva CSME; Department of Pediatrics, Neonatal Intensive Care Unit, Santa Monica Maternity School, Maceio, Alagoas, Brazil., Mariano SCR; Department of Pediatrics, Neonatal Intensive Care Unit, Santa Monica Maternity School, Maceio, Alagoas, Brazil.
Jazyk: angličtina
Zdroj: Surgical neurology international [Surg Neurol Int] 2020 Dec 22; Vol. 11, pp. 448. Date of Electronic Publication: 2020 Dec 22 (Print Publication: 2020).
DOI: 10.25259/SNI_454_2020
Abstrakt: Background: Amniotic band syndrome (ABS) is a rare condition of controversial etiology that is associated with varying degrees of anomalies. This study reports a case of a newborn with ABS associated with double encephalocele in the frontal region.
Case Description: A 29-year-old primiparous woman with no history of prenatal infection or consanguineous marriage had a cesarean section at gestational week 38, giving birth to a newborn who was well but had limb anomalies (constriction rings, amputations, and syndactyly) and craniofacial anomalies, mainly double frontal encephalocele. The patient underwent surgical repair and subsequent placement of a ventriculoperitoneal shunt.
Conclusion: Studies clarifying this uncommon association with double encephalocele are limited. ABS associated with double encephalocele is rare and even more complex when associated with other anomalies. Thus, the conditions in such children are severe and require multidisciplinary monitoring.
Competing Interests: There are no conflicts of interest.
(Copyright: © 2020 Surgical Neurology International.)
Databáze: MEDLINE