| Autor: |
Adachi Y; Department of Hematology, Komaki City Hospital, Japan., Yamazoe-Ishiguri Y; Department of Hematology, Komaki City Hospital, Japan., Iwata S; Department of Hematology, Komaki City Hospital, Japan., Murase A; Department of Hematology, Komaki City Hospital, Japan., Kihara R; Department of Hematology, Komaki City Hospital, Japan., Watamoto K; Department of Hematology, Komaki City Hospital, Japan. |
| Jazyk: |
angličtina |
| Zdroj: |
Internal medicine (Tokyo, Japan) [Intern Med] 2021 Apr 15; Vol. 60 (8), pp. 1271-1277. Date of Electronic Publication: 2020 Nov 09. |
| DOI: |
10.2169/internalmedicine.6032-20 |
| Abstrakt: |
Though adult-onset primary autoimmune pancytopenia (AIP) rarely follows a self-limited course, a standard treatment strategy has not yet been established. We herein report two cases, each involving primary autoimmune neutropenia complicated with autoimmune thrombocytopenia or Evans syndrome. They were refractory to granulocyte-colony stimulating factor, but all lineages of cytopenia promptly recovered with prednisolone (PSL). In case 1, PSL was tapered and discontinued six months after its initiation without AIP relapse. In case 2, PSL has been tapered for five months without relapse. To establish an optimal treatment strategy for AIP, it is necessary to accumulate more cases. |
| Databáze: |
MEDLINE |
| Externí odkaz: |
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