| Autor: |
Kawasaki Y; Division of Cardiology, Children's Hospital of Michigan, Department of Paediatrics, Wayne State University School of Medicine, Detroit, MI, USA.; Division of Paediatric Cardiology, Osaka City General Hospital Paediatric Medical Center, Osaka, Japan., Dentel JN; Division of Cardiovascular Surgery, Children's Hospital of Michigan, Department of Surgery, Wayne State University School of Medicine, Detroit, MI, USA., Walters HL; Division of Cardiovascular Surgery, Children's Hospital of Michigan, Department of Surgery, Wayne State University School of Medicine, Detroit, MI, USA., Galas JM; Division of Cardiology, Children's Hospital of Michigan, Department of Paediatrics, Wayne State University School of Medicine, Detroit, MI, USA., Kobayashi D; Division of Cardiology, Children's Hospital of Michigan, Department of Paediatrics, Wayne State University School of Medicine, Detroit, MI, USA. |
| Abstrakt: |
Total anomalous pulmonary venous connection is a rare congenital heart defect. We report an infant with a mixed form of supracardiac TAPVC, in whom all pulmonary veins, except the right upper, entered a pulmonary venous confluence that is connected to a vertical vein and drained into the superior vena caval-right atrial junction. Several segmental right upper pulmonary veins entered the superior vena cava, superior to the entry of the vertical vein. Surgical repair consisted of the Warden procedure combined with direct anastomosis of the vertical vein to the left atrium. Separate pulmonary venous drainage pathways decreased the risk of post-operative pulmonary venous obstruction. Our patient had an uneventful post-operative course and encouraging 2-month follow-up echocardiography. Careful follow-up is warranted to detect post-operative complications, including obstruction of the pulmonary venous and cavoatrial anastomoses. |
