Combined Nutcracker and Ehlers-Danlos Syndromes: A Case Report.

Autor:	Amato ACM; Department of Vascular Surgery, Amato - Instituto de Medicina Avançada, Av. Brasil 2283, 01431-001, São Paulo, SP, Brazil.; Universidade Santo Amaro (UNISA), R. Isabel Schmidt 349, 04743-030, São Paulo, SP, Brazil., da Silva AEC; Universidade Santo Amaro (UNISA), R. Isabel Schmidt 349, 04743-030, São Paulo, SP, Brazil., Bernal IM; Universidade Santo Amaro (UNISA), R. Isabel Schmidt 349, 04743-030, São Paulo, SP, Brazil., de Oliveira JC; Universidade Santo Amaro (UNISA), R. Isabel Schmidt 349, 04743-030, São Paulo, SP, Brazil., Di Paschoal Almeida Ribeiro M; Universidade Santo Amaro (UNISA), R. Isabel Schmidt 349, 04743-030, São Paulo, SP, Brazil., Schinzari PS; Universidade Santo Amaro (UNISA), R. Isabel Schmidt 349, 04743-030, São Paulo, SP, Brazil., Dos Santos RV; Department of Vascular Surgery, Amato - Instituto de Medicina Avançada, Av. Brasil 2283, 01431-001, São Paulo, SP, Brazil.; Universidade Santo Amaro (UNISA), R. Isabel Schmidt 349, 04743-030, São Paulo, SP, Brazil.
Jazyk:	angličtina
Zdroj:	EJVES vascular forum [EJVES Vasc Forum] 2020 Feb 27; Vol. 47, pp. 12-17. Date of Electronic Publication: 2020 Feb 27 (Print Publication: 2020).
DOI:	10.1016/j.ejvsvf.2020.02.005
Abstrakt:	Introduction: Nutcracker syndrome refers to the clinical manifestations of left renal vein compression between the superior mesenteric artery and the abdominal aorta, causing urinary changes and low back pain. Report: A 44 year old woman presented with low back and pelvic pain. Following the diagnosis of nutcracker syndrome, she underwent endovascular treatment with renal vein stent placement; however, the patient continued to complain of pain. Further examinations revealed left renal vein compression by the portal vein. The patient underwent a second procedure; however, improvement was temporary and her pain returned. Further investigation revealed previously undetected nephroptosis and hyperelasticity. A diagnosis of Ehlers-Danlos syndrome made, possibly explaining the mobility of viscera and unusual compression of the left renal vein by the portal vein. Conclusion: Ehlers-Danlos syndrome can cause nutcracker syndrome and may give rise to visceral pain of mixed origin. Competing Interests: None. (© 2020 The Author(s).)
Databáze:	MEDLINE
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