Ebstein's anomaly presenting with the acute coronary syndrome-a rare combination.

Autor: Trivedi JK; Department of CT Surgery, Apollo Hospitals, Health City, Arilova, Vishakhapatnam, Andhra Pradesh PIN-530040 India., Mahapatra RP; Department of CT Surgery, Apollo Hospitals, Health City, Arilova, Vishakhapatnam, Andhra Pradesh PIN-530040 India., Gandham RK; Department of CT Surgery, Apollo Hospitals, Health City, Arilova, Vishakhapatnam, Andhra Pradesh PIN-530040 India., Ramakrishna GV; Department of CT Surgery, Apollo Hospitals, Health City, Arilova, Vishakhapatnam, Andhra Pradesh PIN-530040 India., Satapathy SK; Department of CT Surgery, Apollo Hospitals, Health City, Arilova, Vishakhapatnam, Andhra Pradesh PIN-530040 India., Mohanty SK; Department of CT Surgery, Apollo Hospitals, Health City, Arilova, Vishakhapatnam, Andhra Pradesh PIN-530040 India., Suresh A; Department of CT Surgery, Apollo Hospitals, Health City, Arilova, Vishakhapatnam, Andhra Pradesh PIN-530040 India.
Jazyk: angličtina
Zdroj: Indian journal of thoracic and cardiovascular surgery [Indian J Thorac Cardiovasc Surg] 2020 Jan; Vol. 36 (1), pp. 56-59. Date of Electronic Publication: 2019 Aug 02.
DOI: 10.1007/s12055-019-00840-z
Abstrakt: Ebstein's anomaly is a relatively rare congenital heart disorder characterised by downward displacement of septal and posterior leaflets of the tricuspid valve into the right ventricle cavity. The usual presenting symptoms are cyanosis, right-sided heart failure and arrhythmia. Progressive heart failure or tachyarrhythmia may worsen cyanosis. The acute coronary syndrome is rarely reported in Ebstein's anomaly. We report a patient of undiagnosed Ebstein's anomaly who was apparently asymptomatic but presented with the acute coronary syndrome. This case report deals with a rare combination of congenital heart disease (Ebstein's anomaly) and coronary artery disease. Ebstein's anomaly (EA) has a prevalence of 1% of all congenital heart diseases, and little evidence is reported in the literature where EA along with coronary artery disease (CAD) exists in individuals less than 45 years old. Therefore, this case report brings attention to the rarity of those pathologies, which individually are already considered rare. And in this case, the association turns this diagnosis exceptional and highlights the complexity of the treatment.
Competing Interests: Conflict of interestDr. Jaideep Kumar Trivedi is not a recipient of any research scholarship. The authors declare that they have no conflict of interest.
(© Indian Association of Cardiovascular-Thoracic Surgeons 2019.)
Databáze: MEDLINE
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