Long QT syndrome with AV Wenckebaching & bundle branch block in a neonate.

Autor: Relan J; All India Institute of Medical Sciences (AIIMS), New Delhi, India. Electronic address: jay_relan_1990@yahoo.co.in., Gujral JS; All India Institute of Medical Sciences (AIIMS), New Delhi, India. Electronic address: jaskarangujral@gmail.com., Reddy SS; All India Institute of Medical Sciences (AIIMS), New Delhi, India. Electronic address: seemala123@gmail.com., Parakh N; All India Institute of Medical Sciences (AIIMS), New Delhi, India. Electronic address: neerajparakh@yahoo.com., Singh S; All India Institute of Medical Sciences (AIIMS), New Delhi, India. Electronic address: sunnyaiims@gmail.com., Ramakrishnan S; All India Institute of Medical Sciences (AIIMS), New Delhi, India. Electronic address: ramaaiims@gmail.com.
Jazyk: angličtina
Zdroj: Indian pacing and electrophysiology journal [Indian Pacing Electrophysiol J] 2020 Nov - Dec; Vol. 20 (6), pp. 286-289. Date of Electronic Publication: 2020 Aug 06.
DOI: 10.1016/j.ipej.2020.07.005
Abstrakt: We present a case of 21-day-old neonate brought with history of 3 episodes of syncope. Evaluation revealed congenital long QT syndrome associated with long cycle atypical AV Wenkebaching with a long short cycle sequence related left bundle branch aberrancy. Syncope was attributed to multiple episodes of Torsades de Pointes, necessitating emergency epicardial pacemaker implantation. In addition, child was started on oral propranolol therapy. On 2 months follow up, child was stable with no ventricular high rate episodes during pacemaker interrogation.
Competing Interests: Declaration of competing interest ‘The Author(s) declare(s) that there is no conflict of interest’ “All authors have read and approved the manuscript."
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Databáze: MEDLINE