Undiagnosed Systemic Mastocytosis Presenting as Postoperative Distributive Shock: A Case Report.

Autor: Ripoll JG; From the Department of Anesthesiology and Perioperative Medicine., Ritter MJ; From the Department of Anesthesiology and Perioperative Medicine.; Division of Critical Care Medicine.; Division of Cardiovascular Anesthesia., Comfere TB; From the Department of Anesthesiology and Perioperative Medicine.; Division of Critical Care Medicine., Smith MM; From the Department of Anesthesiology and Perioperative Medicine.; Division of Cardiovascular Anesthesia., Schaff HV; Division of Cardiothoracic Surgery, Mayo Clinic, Rochester, Minnesota., Gilkey GD; From the Department of Anesthesiology and Perioperative Medicine.; Division of Cardiovascular Anesthesia., Warner MA; From the Department of Anesthesiology and Perioperative Medicine.; Division of Critical Care Medicine.
Jazyk: angličtina
Zdroj: A&A practice [A A Pract] 2019 Nov 15; Vol. 13 (10), pp. 392-395.
DOI: 10.1213/XAA.0000000000001093
Abstrakt: Systemic mastocytosis (SM) is a rare clinical condition resulting from a clonal proliferation of abnormal mast cells. The clinical presentation may vary from mild cutaneous manifestations to aggressive systemic symptoms including intermittent episodes of anaphylaxis. We present a case of a 69-year-old male with abrupt and recurrent episodes of anaphylaxis with refractory distributive shock following cardiac surgery with cardiopulmonary bypass. Following a complex postoperative course, a bone marrow biopsy ultimately confirmed the diagnosis. Although rare, SM should be considered in the differential diagnosis of postoperative patients with unexplained and recurrent episodes of distributive shock.
Databáze: MEDLINE