Living Donor Kidney Transplantation in a Patient With Epidermolysis Bullosa: A Case Report.

Autor: Ceuppens SHE; Department of Surgery, Division of HPB & Transplant Surgery, Erasmus MC, Rotterdam, the Netherlands., Kimenai HJAN; Department of Surgery, Division of HPB & Transplant Surgery, Erasmus MC, Rotterdam, the Netherlands., Roodnat JI; Department of Internal Medicine, Erasmus MC, Rotterdam, the Netherlands., Mertens Zur Borg IRAM; Department of Anaesthesiology, Erasmus MC, Rotterdam, the Netherlands., Duipmans JC; Department of Dermatology, University Medical Center Groningen, the Netherlands., IJzermans JNM; Department of Surgery, Division of HPB & Transplant Surgery, Erasmus MC, Rotterdam, the Netherlands., Minnee RC; Department of Surgery, Division of HPB & Transplant Surgery, Erasmus MC, Rotterdam, the Netherlands. Electronic address: r.minnee@erasmusmc.nl.
Jazyk: angličtina
Zdroj: Transplantation proceedings [Transplant Proc] 2019 Nov; Vol. 51 (9), pp. 3074-3076. Date of Electronic Publication: 2019 Jul 19.
DOI: 10.1016/j.transproceed.2019.04.049
Abstrakt: Severe recessive dystrophic epidermolysis bullosa is a very rare inherited disease with excessive blisters forming starting at birth. Surgical intervention in this population creates a challenge: preventing formation of new lesions while managing previously scarred tissues. We present a case of a 27-year-old patient with end-stage renal disease caused by rapidly progressive IgA nephropathy. Living donor kidney transplantation was performed under local, spinal and epidural anesthesia. Living kidney transplantation in epidermolysis bullosa patients with end-stage renal disease should not be a contraindication for transplantation and should be considered as a viable and feasible option after careful preparation.
(Copyright © 2019 Elsevier Inc. All rights reserved.)
Databáze: MEDLINE
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