[Amniotic band syndrome: prenatal diagnosis and management challenges (about 2 cases of lethal malformations)].
Autor: | Adadi H; Service Gynécologie Obstétrique II, CHU Hassan II, Fès, Maroc., Chaara H; Service Gynécologie Obstétrique II, CHU Hassan II, Fès, Maroc., Attar I; Service Gynécologie Obstétrique II, CHU Hassan II, Fès, Maroc., Jayi S; Service Gynécologie Obstétrique II, CHU Hassan II, Fès, Maroc., Alaoui FF; Service Gynécologie Obstétrique II, CHU Hassan II, Fès, Maroc., Melhouf MA; Service Gynécologie Obstétrique II, CHU Hassan II, Fès, Maroc. |
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Jazyk: | francouzština |
Zdroj: | The Pan African medical journal [Pan Afr Med J] 2019 Mar 13; Vol. 32, pp. 116. Date of Electronic Publication: 2019 Mar 13 (Print Publication: 2019). |
DOI: | 10.11604/pamj.2019.32.116.18048 |
Abstrakt: | Amniotic band syndrome (ABS) comprises of a spectrum of complex congenital malformations mainly interesting the limbs, but even the craniofacial region and the thoracoabdominal axis. There are two major opposing pathophysiological theories: premature rupture of the amniotic sac (exogenous growth theory) would result in the formation of fibrous bands which would lead to strangulation, thus causing the observed abnormalities; the endogenous theory holds that this is a syndrome of vascular origin and that the bands have no causative role. Prognosis depends on the severity of malformations. We here report two cases of lethal malformations in order to discuss the challenges in the diagnosis and treatment of amniotic band syndrome. This study mainly aims to highlight the role of prenatal diagnosis in the therapeutic management of this embryo-fetopathy. Competing Interests: Les auteurs ne déclarent aucun conflit d'intérêts. |
Databáze: | MEDLINE |
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