| Autor: |
Cerejo RPS; Cardiothoracic Surgery Department, Hospital de Santa Marta-Centro Hospitalar Lisboa Central, Lisbon, Portugal., Rodrigues RAN; Cardiothoracic Surgery Department, Hospital de Santa Marta-Centro Hospitalar Lisboa Central, Lisbon, Portugal., Martins JD; Pediatric Cardiology Department, Hospital de Santa Marta-Centro Hospitalar Lisboa Central, Lisbon, Portugal., Torres CGEC; Thoracic Surgery Department, Hospital Pulido Valente-Centro Hospitalar Lisboa Norte, Lisbon, Portugal., Sousa LM; Cardiology Department, Hospital de Santa Marta-Centro Hospitalar Lisboa Central, Lisbon, Portugal., Pinto FF; Pediatric Cardiology Department, Hospital de Santa Marta-Centro Hospitalar Lisboa Central, Lisbon, Portugal., Fragata JIG; Cardiothoracic Surgery Department, Hospital de Santa Marta-Centro Hospitalar Lisboa Central, Lisbon, Portugal. |
| Abstrakt: |
Hutchinson-Gilford progeria syndrome is a rare genetic disorder, characterized by progressive premature aging and early death in the first or second decade of life, usually secondary to cardiovascular events (myocardial infarction and stroke). We report a case of a 14-year-old boy with progeria syndrome and cardiac arrest due to myocardial infarction, who was submitted to an immediate coronary angiography which revealed left main stem and three-vessel coronary artery disease. A prompt double bypass coronary artery grafting surgery was performed, and, despite successful coronary reperfusion, the patient remained in coma and brain death was declared on fourth day after surgery. |
