[IgG4 related disease with exclusive sinonasal involvement: A case report and literature review].

Autor: García-Curdi F; Servicio de Otorrinolaringología, Hospital Clínico Universitario Lozano Blesa, Zaragoza, España. Electronic address: fgcurdi@gmail.com., Lois-Ortega Y; Servicio de Otorrinolaringología, Hospital Clínico Universitario Lozano Blesa, Zaragoza, España., Gonzales-Sejas AG; Servicio de Anatomía Patológica, Hospital Clínico Universitario Lozano Blesa, Zaragoza, España., Alfonso-Collado JI; Servicio de Otorrinolaringología, Hospital Clínico Universitario Lozano Blesa, Zaragoza, España., Fumanal-Senz L; Servicio de Otorrinolaringología, Hospital Clínico Universitario Lozano Blesa, Zaragoza, España., Vallés-Varela H; Servicio de Otorrinolaringología, Hospital Clínico Universitario Lozano Blesa, Zaragoza, España.
Jazyk: Spanish; Castilian
Zdroj: Revista espanola de patologia : publicacion oficial de la Sociedad Espanola de Anatomia Patologica y de la Sociedad Espanola de Citologia [Rev Esp Patol] 2019 Apr - Jun; Vol. 52 (2), pp. 125-129. Date of Electronic Publication: 2018 Jul 04.
DOI: 10.1016/j.patol.2018.05.002
Abstrakt: IgG4 related disease (igG4-RD) is a pathological process which integrates a large number of diseases of unknown pathogenesis, considered as being exclusive to many different organs. Diagnosis is established through histological, radiological and serological criteria. Treatment is based on long term corticosteroids; rituximab being used only in refractory cases. It is unusual for this entity to be found exclusively in the head and neck, without systemic involvement; there are only a few reported cases to date. We present a case of a nasosinusal IgG4-RD orbital tumor with paranasal sinus involvement. The accurate diagnosis made early onset corticosteroid treatment possible and the patient is currently asymptomatic.
(Copyright © 2018 Sociedad Española de Anatomía Patológica. Publicado por Elsevier España, S.L.U. All rights reserved.)
Databáze: MEDLINE
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