Anesthesia in a pediatric patient with ROHADD syndrome.

Autor: Esparza Isasa E; Servicio de Anestesiología y Reanimación, Hospital Universitario Ramón y Cajal, Madrid, España., Palomero Rodríguez MA; Servicio de Anestesiología y Reanimación, Hospital Universitario Ramón y Cajal, Madrid, España. Electronic address: mapalomero@gmail.com., Acebedo Bambaren I; Servicio de Anestesiología y Reanimación, Hospital Universitario Ramón y Cajal, Madrid, España., Medrano Viñas C; Servicio de Anestesiología y Reanimación, Hospital Universitario Ramón y Cajal, Madrid, España., Gil Mayo D; Servicio de Anestesiología y Reanimación, Hospital Universitario Ramón y Cajal, Madrid, España., Domínguez Pérez F; Servicio de Anestesiología y Reanimación, Hospital Universitario Ramón y Cajal, Madrid, España., Pestaña Lagunas D; Servicio de Anestesiología y Reanimación, Hospital Universitario Ramón y Cajal, Madrid, España.
Jazyk: English; Spanish; Castilian
Zdroj: Revista espanola de anestesiologia y reanimacion [Rev Esp Anestesiol Reanim (Engl Ed)] 2018 Nov; Vol. 65 (9), pp. 525-529. Date of Electronic Publication: 2018 May 01.
DOI: 10.1016/j.redar.2018.03.005
Abstrakt: Rapid-onset obesity with hypothalamic dysfunction, hypoventilation, and autonomic dysregulation (ROHHAD) syndrome is a rare entity that is characterised by its onset in healthy children at 2-4 years of age. It is a complex syndrome that includes, among other symptoms, rapid weight gain with hyperphagia, hypothalamic dysfunction, central hypoventilation, and autonomic dysregulation. The case is presented of a 10-year-old boy with a diagnosis of ROHHAD syndrome undergoing insertion of a port-a-cath under general anaesthesia, who developed complications during the anaesthetic procedure related to his illness. The peri-operative management of these patients represents a challenge for the anaesthetist, given the involvement of multiple systems and the frequent respiratory comorbidities associated with them. A summary is presented of some of the implications and anaesthetic considerations that must be taken into account in the management of these patients.
(Copyright © 2018 Sociedad Española de Anestesiología, Reanimación y Terapéutica del Dolor. Publicado por Elsevier España, S.L.U. All rights reserved.)
Databáze: MEDLINE
Externí odkaz: