IgG4-related sclerosing mesenteritis, a rare condition that causes abdominal pain.

Autor: Mejías Manzano MLÁ; Unidad de Gestión Clínica de Aparato Digestivo, Hospital Universitario Virgen del Rocío, España., Trigo Salado C; Unidad de Gestión Clínica de Aparato Digestivo, Hospital Universitario Virgen del Rocío, España., Serrano Jiménez M; Anatomía Patológica, Hospitales Universitarios Virgen del Rocío. , España., Parada Blázquez MJ; Radiodiagnóstico, Hospital Universitario Virgen del Rocio, España., Leo Carnerero E; Unidad de Gestión Clínica de Aparato Digestivo, Hospital Universitario Virgen del Rocío, España.
Jazyk: angličtina
Zdroj: Revista espanola de enfermedades digestivas [Rev Esp Enferm Dig] 2018 Mar; Vol. 110 (3), pp. 201-203.
DOI: 10.17235/reed.2017.5228/2017
Abstrakt: The identification of IgG4-related disease as a distinct immune-mediated condition encompassing disorders that were traditionally seen as idiopathic has been a revolution in the diagnostic and therapeutic algorithm in several medical fields. This condition usually involves multiple organs (isolated organ involvement is uncommon except in the pancreas) with characteristic histopathological findings. We report a case that was assessed due to abdominal pain and subsequently diagnosed with IgG4-related sclerosing mesenteritis. A comprehensive work-up of the case ruled out other conditions and a diagnosis of IgG4-related sclerosing mesenteritis was made according to radiographic and histopathological criteria.
Databáze: MEDLINE