Cardiac arrest related to anaesthesia in Williams-Beuren syndrome.

Autor: Lucena Delgado J; Departamento de Anestesiología, Reanimación y Terapéutica del Dolor, Hospital Universitario La Paz, Madrid, España. Electronic address: jldfisio@msn.com., Sanabria Carretero P; Departamento de Anestesiología Pediátrica, Reanimación y Terapéutica del Dolor, Hospital Universitario La Paz, Madrid, España., Durán la Fuente P; Departamento de Anestesiología Pediátrica, Reanimación y Terapéutica del Dolor, Hospital Universitario La Paz, Madrid, España., Gónzalez Rocafort A; Departamento de Cirugía Cardíaca Pediátrica, Hospital Universitario La Paz, Madrid, España., Castro Parga L; Departamento de Anestesiología Pediátrica, Reanimación y Terapéutica del Dolor, Hospital Universitario La Paz, Madrid, España., Reinoso Barbero F; Departamento de Anestesiología Pediátrica, Reanimación y Terapéutica del Dolor, Hospital Universitario La Paz, Madrid, España.
Jazyk: English; Spanish; Castilian
Zdroj: Revista espanola de anestesiologia y reanimacion [Rev Esp Anestesiol Reanim (Engl Ed)] 2018 Apr; Vol. 65 (4), pp. 234-237. Date of Electronic Publication: 2017 Dec 13.
DOI: 10.1016/j.redar.2017.11.005
Abstrakt: Williams-Beuren syndrome is the clinical manifestation of a congenital genetic disorder in the elastin gene, among others. There is a history of cardiac arrest refractory to resuscitation manoeuvres in anaesthesia. The incidence of myocardial ischaemia is high during anaesthetic induction, but there are patients who do not have this condition yet also have had very serious cardiac events, and issues that are still to be resolved. Case descriptions will enable the common pathophysiological factors to be defined, and decrease morbidity and mortality. We report the case of a 3-year-old boy with cardiac arrest at induction, rescued with circulatory assistance with extracorporeal membrane oxygenation and hypothermia induced for cerebral protection.
(Copyright © 2017 Sociedad Española de Anestesiología, Reanimación y Terapéutica del Dolor. Publicado por Elsevier España, S.L.U. All rights reserved.)
Databáze: MEDLINE
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