Single-Ventricle Palliation in a 4-Year-Old With Ehlers-Danlos Syndrome.
| Autor: | DeBoard ZM; Division of Cardiothoracic Surgery, University of Utah, Salt Lake City, Utah. Electronic address: zdeboard@hsc.utah.edu., Eckhauser AW; Pediatric Cardiothoracic Surgery, Primary Children's Medical Center, Salt Lake City, Utah., Griffiths E; Pediatric Cardiothoracic Surgery, Primary Children's Medical Center, Salt Lake City, Utah. |
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| Jazyk: | angličtina |
| Zdroj: | The Annals of thoracic surgery [Ann Thorac Surg] 2018 Jan; Vol. 105 (1), pp. e31-e32. |
| DOI: | 10.1016/j.athoracsur.2017.08.027 |
| Abstrakt: | We report the case of a 4-year-old boy with Ehlers-Danlos syndrome undergoing single-ventricle palliation for an unbalanced atrioventricular canal defect. No reports of single-ventricle palliation in the setting of connective tissue disorders exist in the current literature. Unique findings on the patient's preoperative imaging included a disproportionately large neoaortic root and a regurgitant atrioventricular valve, which may foretell the need for future intervention. (Copyright © 2018 The Society of Thoracic Surgeons. Published by Elsevier Inc. All rights reserved.) |
| Databáze: | MEDLINE |
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