Dermatofibrosarcoma protuberans coexisting in a patient with a vascular malformation-a rare coincidence.

Autor: Deskoulidi P; Department of Plastic Surgery, St. Savvas Cancer Hospital of Athens, 171 Alexandras Avenue, Athens 11522, Greece., Sofopoulos M; Department of Surgical Pathology, St. Savvas Cancer Hospital of Athens, 171 Alexandras Avenue, Athens 11522, Greece., Diamantopoulos P; Department of Plastic Surgery, St. Savvas Cancer Hospital of Athens, 171 Alexandras Avenue, Athens 11522, Greece., Nikolaidou T; Department of Plastic Surgery, St. Savvas Cancer Hospital of Athens, 171 Alexandras Avenue, Athens 11522, Greece., Maltzaris N; Department of Plastic Surgery, St. Savvas Cancer Hospital of Athens, 171 Alexandras Avenue, Athens 11522, Greece., Theodorakopoulou M; Department of Surgical Pathology, St. Savvas Cancer Hospital of Athens, 171 Alexandras Avenue, Athens 11522, Greece., Klonaris C; Vascular Surgery Unit, Laiko General Hospital of Athens, Agiou Thoma17, Athens 11527, Greece., Arnogiannaki N; Department of Surgical Pathology, St. Savvas Cancer Hospital of Athens, 171 Alexandras Avenue, Athens 11522, Greece., Kotrotsiou M; Department of Plastic Surgery, Evangelismos General Hospital of Athens, Ipsilantou 45-47, Athens 106 76, Greece., Stavrianos S; Department of Plastic Surgery, St. Savvas Cancer Hospital of Athens, 171 Alexandras Avenue, Athens 11522, Greece.
Jazyk: angličtina
Zdroj: Journal of surgical case reports [J Surg Case Rep] 2017 Oct 09; Vol. 2017 (10), pp. rjx192. Date of Electronic Publication: 2017 Oct 09 (Print Publication: 2017).
DOI: 10.1093/jscr/rjx192
Abstrakt: Dermatofibrosarcoma protuberans with fibrosarcomatous differentiation (DFSP-FS) is a rare soft tissue tumor with more aggressive behavior and it is not clear what causes this type of skin cancer. We describe the case of a 48-year-old woman who was born with a vascular malformation in the sternal region and presented suddenly with a soft tissue sarcoma (DFSP-FS) in the same territory. She was initially treated by embolization as the sarcoma was misdiagnosed but the tumor within 6 months seemed to be growing rapidly and reached a giant dimension with ulceration and required surgical intervention. The patient underwent a surgical removal of the mass but as the pathology report included a DFSP-FS with close margins,a second operation was required. A wide local excision was performed and reconstruction of defect by using bilateral pectoralis major muscle flaps and a full thickness skin graft from the abdominal wall. Post operatively the patient was treated with radiotherapy.
Databáze: MEDLINE
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