Outcome of Combined Mitral and Aortic Valve Replacement in Adults With Mucopolysaccharidosis (the Hurler Syndrome).

Autor: Robinson CR; Baylor Heart and Vascular Institute, Departments of Pathology and Internal Medicine (Division of Cardiology), Baylor University Medical Center at Dallas, Baylor Scott & White Health, Dallas, Texas., Roberts WC; Baylor Heart and Vascular Institute, Departments of Pathology and Internal Medicine (Division of Cardiology), Baylor University Medical Center at Dallas, Baylor Scott & White Health, Dallas, Texas. Electronic address: william.roberts1@bswhealth.org.
Jazyk: angličtina
Zdroj: The American journal of cardiology [Am J Cardiol] 2017 Dec 01; Vol. 120 (11), pp. 2113-2118. Date of Electronic Publication: 2017 Aug 12.
DOI: 10.1016/j.amjcard.2017.08.001
Abstrakt: We describe 2 adult sisters with type I mucopolysaccharidosis (MPS) who underwent combined mitral and aortic valve replacement for mitral and aortic valve stenosis. One died early postoperatively and the other survived but had a repeat double-valve replacement 1 month after the first. We analyzed previously reported patients with MPS and valve replacement to learn of their outcomes. The study of our 2 patients and those previously reported suggests that valve replacement in patients with MPS should be viewed with extreme caution.
(Copyright © 2017 Elsevier Inc. All rights reserved.)
Databáze: MEDLINE
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