Spectrum of MRI Appearance of Mayer-Rokitansky-Kuster-Hauser (MRKH) Syndrome in Primary Amenorrhea Patients.

Autor:	Boruah DK; Assistant Professor, Department of Radiodiagnosis, Assam Medical College, Dibrugarh, Assam, India., Sanyal S; Consultant Radiologist, Department of Radiodiagnosis, Airedale General Hospital, Keighley, West Yorkshire, United kingdom., Gogoi BB; Senior Resident, Department of Pathology, NEIGHR MS, Shillong, Meghalaya, India., Mahanta K; Postgraduate Student, Department of Radiodiagnosis, Assam Medical College, Dibrugarh, Assam, India., Prakash A; Assistant Professor, Department of Radiodiagnosis, Bangalore Medical College, Bengaluru, Karnataka, India., Augustine A; Postgraduate Student, Department of Radiodiagnosis, Assam Medical College, Dibrugarh, Assam, India., Achar S; Postgraduate Student, Department of Radiodiagnosis, Assam Medical College, Dibrugarh, Assam, India., Baishya H; Postgraduate Student, Department of Radiodiagnosis, Assam Medical College, Dibrugarh, Assam, India.
Jazyk:	angličtina
Zdroj:	Journal of clinical and diagnostic research : JCDR [J Clin Diagn Res] 2017 Jul; Vol. 11 (7), pp. TC30-TC35. Date of Electronic Publication: 2017 Jul 01.
DOI:	10.7860/JCDR/2017/29016.10317
Abstrakt:	Introduction: Mayer-Rokitansky-Kuster-Hauser (MRKH) synd-rome is a malformation in female genital tract due to interrupted embryonic development of para-mesonephric ducts leading to uterine and proximal vagina aplasia or hypoplasia. Aim: To analyse the MRI findings in females suspected of MRKH syndrome in a primary amenorrhea workup. Materials and Methods: A cross-sectional study comprising of 11 patients of MRKH syndrome presented in a tertiary care centre from March 2016 to February 2017 evaluated in 1.5 Tesla MRI scanner. Results: Normal positioned small vestigial uterus demonstrated in two patients (18.2%) and complete uterine and proximal vaginal agenesis were noted in nine patients (81.8%). The mean volume of rudimentary right uterine bud was 2.26 mL ±3.3 (SD) and left uterine bud was 1.27 mL±1.1 (SD). The mean volume of right ovary was 4.74 mL±2.58 (SD) and left ovary was 4.65 mL±2.2 (SD). The mean developed vaginal length was 26.2 mm±6.34 (SD). Conclusion: The rudimentary uterine buds associated with MRKH syndrome always maintained caudal relationship with ovary. Ovaries or rudimentary uterine buds can be ectopic and should be recognized with MRI before undergoing fertility treatment. Following MRI diagnosis, surgery allows patients to have sexual function with possible attainment of reproduction after assisted reproduction technique or surrogacy.
Databáze:	MEDLINE
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