Unrepaired Tetralogy of Fallot with Absent Pulmonary Valve in a Mildly Symptomatic 16-Year-Old Boy.

Autor: Drogalis-Kim DE, Reemtsen BL, Reardon LC
Jazyk: angličtina
Zdroj: Texas Heart Institute journal [Tex Heart Inst J] 2016 Dec 01; Vol. 43 (6), pp. 517-519. Date of Electronic Publication: 2016 Dec 01 (Print Publication: 2016).
DOI: 10.14503/THIJ-15-5385
Abstrakt: Absent pulmonary valve is a rare and severe variant seen in only 3% to 6% of patients with tetralogy of Fallot. Fetuses with this combined condition who survive through birth typically need intervention in infancy or early childhood because of respiratory distress, heart failure, or failure to thrive. We describe the unusual case of a mildly symptomatic 16-year-old boy with these conditions who underwent successful primary repair. Our search of the medical literature yielded fewer than 5 cases of tetralogy of Fallot with absent pulmonary valve (or variants with an absent left pulmonary artery) and survival without repair into later adolescence or adulthood.
Databáze: MEDLINE