Budd-Chiari syndrome associated with coeliac disease: case report and literature review.

Autor: Jadallah KA; Department of Internal Medicine, King Abdullah University Hospital, Irbid, Jordan khaled-j@just.edu.jo., Sarsak EW; Department of Internal Medicine, King Abdullah University Hospital, Irbid, Jordan., Khazaleh YM; Department of Internal Medicine, King Abdullah University Hospital, Irbid, Jordan., Barakat RM; Department of Internal Medicine, King Abdullah University Hospital, Irbid, Jordan.
Jazyk: angličtina
Zdroj: Gastroenterology report [Gastroenterol Rep (Oxf)] 2018 Nov; Vol. 6 (4), pp. 308-312. Date of Electronic Publication: 2016 Sep 07.
DOI: 10.1093/gastro/gow030
Abstrakt: We report a case of Budd-Chiari syndrome occurring in a patient with coeliac disease, who presented with symptoms of increased abdominal girth, right upper quadrant pain and shortness of breath for three weeks prior to admission. Initial assessment revealed the presence of moderate ascites, hepatosplenomegaly and right-sided pleural effusion. Further diagnostic work-up established a diagnosis of chronic Budd-Chiari syndrome. Interestingly, complete screening for pro-thrombotic factors was negative. A review of the literature on this association disclosed only 28 similar cases, with the majority of them describing individuals of North African origin. Interestingly, in the majority of cases no specific thrombotic factor could be identified, suggesting that coeliac disease may play a role in this thrombotic disorder.
(© The Author(s) 2016. Published by Oxford University Press and Sixth Affiliated Hospital of Sun Yat-Sen University.)
Databáze: MEDLINE