Herlyn-Werner-Wunderlich syndrome with a partially obstructed hemivagina.

Autor: Moshiri M, Seyal AR, Cruite I, Bhargava P
Jazyk: angličtina
Zdroj: Radiology case reports [Radiol Case Rep] 2015 Dec 07; Vol. 7 (4), pp. 800. Date of Electronic Publication: 2015 Dec 07 (Print Publication: 2012).
DOI: 10.2484/rcr.v7i4.800
Abstrakt: Uterine didelphys with obstructed hemivagina and ipsilateral renal agenesis is a rare congenital anomaly of the Müllerian duct system referred to as Herlyn-Werner-Wunderlich syndrome. Because of its rare occurrence, a high level of suspicion is often required for diagnosis. Clinically, these patients usually present after menarche with pelvic pain, dysmenorrhea, and a palpable pelvic mass. We present a case of a 31-year-old female patient with infertility. Imaging findings were consistent with Herlyn-Werner-Wunderlich syndrome, with a congenital defect in the longitudinal vaginal septum resulting in partial spontaneous decompression of right-sided hematocolpos.
Databáze: MEDLINE