[The differential diagnosis of Erdheim-Chester disease and IgG4-related diseases].

Autor: Vasilyev VI; V.A. Nasonova Research Institute of Rheumatology, Moscow, Russia., Sokol EV; V.A. Nasonova Research Institute of Rheumatology, Moscow, Russia., Kokosadze NV; N.N. Blokhin Russian Cancer Research Center, Ministry of Health of Russia, Moscow, Russia., Pavlovskaya AI; N.N. Blokhin Russian Cancer Research Center, Ministry of Health of Russia, Moscow, Russia., Komov DV; N.N. Blokhin Russian Cancer Research Center, Ministry of Health of Russia, Moscow, Russia., Palshina SG; V.A. Nasonova Research Institute of Rheumatology, Moscow, Russia., Mukhortova OV; A.N. Bakulev Research Center of Cardiovascular Surgery, Moscow, Russia., Safonova TN; Research Institute of Eye Diseases, Moscow, Russia.
Jazyk: ruština
Zdroj: Terapevticheskii arkhiv [Ter Arkh] 2016; Vol. 88 (5), pp. 70-76.
DOI: 10.17116/terarkh201688570-76
Abstrakt: The paper describes Russia's first diagnosed case of Erdheim--Chester disease (systemic histiocytosis) in a 65-year-old man who has been long treated for Ormond's disease (idiopathic retroperitoneal fibrosis). It also gives the data available in the literature on the pathogenetic components of these diseases and on the similarity of many clinical, laboratory, and morphological characteristics of these two immunoinflammatory diseases and covers the issues of their differential diagnosis. Invasive procedures with a careful morphological/immunomorphological examination of biopsy specimens obtained from affected tissues are shown to be necessary for accurate diagnosis.
Databáze: MEDLINE