Non-Trigger Anesthesia Management in a Patient With Leigh's Syndrome Presenting for Dental Rehabilitation.

Autor: Suleman MI; Division of Pediatric Anesthesia, Arkansas Children's Hospital, Arkansas, USA., Edala T; Department of Anesthesiology, University of Arkansas for Medical Sciences, Arkansas, USA., Abraham E; Division of Pediatric Anesthesia, Arkansas Children's Hospital, Arkansas, USA., Siddiqu MS; Division of Pediatric Anesthesia, Arkansas Children's Hospital, Arkansas, USA.
Jazyk: angličtina
Zdroj: Anesthesiology and pain medicine [Anesth Pain Med] 2015 Nov 30; Vol. 5 (6), pp. e28804. Date of Electronic Publication: 2015 Nov 30 (Print Publication: 2015).
DOI: 10.5812/aapm.28804
Abstrakt: Introduction: Usually presenting in infancy, Leigh's syndrome is an inherited condition often manifesting with seizures, ataxia, developmental delay, and dysarthria. The disorder is rare, appearing in approximately 1 in 40,000 live births. Consequently, providing these patients with a suitable plan by which to administer anesthetics remains problematic.
Case Presentation: We report a male patient with Leigh's syndrome and a family history suggestive of unknown hypotonia and malignant hyperthermia presenting for dental rehabilitation.
Conclusions: Dexmedetomidine with remifentanil can be used with no complication in this senerio.
Databáze: MEDLINE