| Autor: |
Forman AB; Division of Dermatology, Children's Memorial Hospital, Chicago, Illinois., Prendiville JS, Esterly NB, Hebert AA, Duvic M, Horiguchi Y, Fine JD |
| Jazyk: |
angličtina |
| Zdroj: |
Pediatric dermatology [Pediatr Dermatol] 1989 Jun; Vol. 6 (2), pp. 91-101. |
| DOI: |
10.1111/j.1525-1470.1989.tb01004.x |
| Abstrakt: |
We evaluated two patients with hereditary bullous poikiloderma. Both had acral bullae, generalized poikiloderma with prominent atrophy, and acral keratoses. One patient, with sporadic disease, had, in addition, urethral and subglottic stenoses, webbing of digits, and poor dentition. The other patient, whose disease was dominantly inherited, had koilonychia. The results of cutaneous histopathology, electron microscopy, and immunofluorescence mapping studies are presented. It is possible that Kindler syndrome and Weary's hereditary acrokeratotic poikiloderma are variants of the same disease. |
| Databáze: |
MEDLINE |
| Externí odkaz: |
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