Plummer-Vinson Syndrome in Children.

Autor: Butori M; Departments of Pediatric Digestive and Respiratory Diseases †Radiology, Robert-Debré Hospital, Assistance Publique-Hôpitaux de Paris, Paris, France., Mahmoudi S, Dugelay-Ecochard E, Belarbi N, Bellaïche M, Hugot JP, Viala J
Jazyk: angličtina
Zdroj: Journal of pediatric gastroenterology and nutrition [J Pediatr Gastroenterol Nutr] 2015 Nov; Vol. 61 (5), pp. 547-52.
DOI: 10.1097/MPG.0000000000000842
Abstrakt: Objectives: Plummer-Vinson syndrome (PVS), also called Kelly-Paterson syndrome, is a rare cause of dysphagia in children. This syndrome associates single or multiple webs in the upper esophagus with frequent iron deficiency.
Methods: We reported 3 pediatric cases of PVS before analyzing all of the cases of PVS in children reported in the PubMed and EMBASE databases.
Results: Among 17 reported PVS cases in children, all of the patients experienced iron-deficiency anemia, and no immunological disease was reported. The male/female ratio was 1/1.9, and most cases were observed in adolescents. Conversely to adults, endoscopic dilation was often necessary because dysphagia resisted iron supplementation. A single dilation was usually sufficient. One case of pediatric PVS experienced esophageal cancer in adulthood.
Conclusions: In the case of dysphagia in children, a swallow barium exploration with lateral incidence should look for PVS. Conversely to adults, an endoscopic dilation is frequently necessary to control dysphagia in children.
Databáze: MEDLINE
Externí odkaz: