| Autor: |
Orsini M; Centro Universitário Augusto Motta, Rio de Janeiro, RJ, BR., Lopes AJ; Centro Universitário Augusto Motta, Rio de Janeiro, RJ, BR., Menezes SL; Centro Universitário Augusto Motta, Rio de Janeiro, RJ, BR., Oliveira AB; Departamento de Neurologia, Universidade Federal de São Paulo, São Paulo, SP, BR., Freitas MR; Departamento de Neurologia, Universidade Federal Fluminense, Niteroi, RJ, BR., Nascimento OJ; Departamento de Neurologia, Universidade Federal Fluminense, Niteroi, RJ, BR., Guimarães FS; Centro Universitário Augusto Motta, Rio de Janeiro, RJ, BR. |
| Abstrakt: |
Amyotrophic lateral sclerosis is a progressive neuromuscular disease, resulting in respiratory muscle weakness, reduced pulmonary volumes, ineffective cough, secretion retention, and respiratory failure. Measures as vital capacity, maximal inspiratory and expiratory pressures, sniff nasal inspiratory pressure, cough peak flow and pulse oximetry are recommended to monitor the respiratory function. The patients should be followed up by a multidisciplinary team, focused in improving the quality of life and deal with the respiratory symptoms. The respiratory care approach includes airway clearance techniques, mechanically assisted cough and noninvasive mechanical ventilation. Vaccination and respiratory pharmacological support are also recommended. To date, there is no enough evidence supporting the inspiratory muscle training and diaphragmatic pacing. |
