Valve Sparing Aortic Root Replacement in Children with Loeys-Dietz Syndrome.
| Autor: | Sim HT; Department of Thoracic and Cardiovascular Surgery, Saint Carollo General Hospital., Seo DJ; Division of Pediatric Cardiac Surgery, Asan Medical Center, University of Ulsan College of Medicine., Yu JJ; Division of Pediatric Cardiology, Asan Medical Center, University of Ulsan College of Medicine., Baek JS; Division of Pediatric Cardiology, Asan Medical Center, University of Ulsan College of Medicine., Goo HW; Department of Radiology and Research Institute of Radiology, Asan Medical Center, University of Ulsan College of Medicine., Park JJ; Division of Pediatric Cardiac Surgery, Asan Medical Center, University of Ulsan College of Medicine. |
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| Jazyk: | angličtina |
| Zdroj: | The Korean journal of thoracic and cardiovascular surgery [Korean J Thorac Cardiovasc Surg] 2015 Aug; Vol. 48 (4), pp. 272-6. Date of Electronic Publication: 2015 Aug 05. |
| DOI: | 10.5090/kjtcs.2015.48.4.272 |
| Abstrakt: | Loeys-Dietz syndrome (LDS) is an autosomal dominant connective tissue disorder that is characterized by aggressive arterial and aortic disease, often involving the formation of aortic aneurysms. We describe the cases of two children with LDS who were diagnosed with aortic root aneurysms and successfully treated by valve-sparing aortic root replacement (VSRR) with a Valsalva graft. VSRR is a safe and suitable operation for children that avoids prosthetic valve replacement. |
| Databáze: | MEDLINE |
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