Hypohidrotic ectodermal dysplasia: a clinical case with a longitudinal approach.

Autor:	Fraiz FC; Associate Professor, Department of Stomatology, Avenida Prefeito Lothario Meissner 632, Jardim Botânico, Curitiba, ParanáBrazil, Zip Code: 80210-170, Phone: 55 41 3360 4021, e-mail: fabianfraiz@gmail.com., Gugisch RC; Associate Professor, Department of Stomatology, Universidade Federal do Paraná, Paraná, Brazil., Cavalcante-Leão BL; MSc Student, Department of Stomatology, Universidade Federal do Paraná, Paraná, Brazil., Macedo LM; Pediatric Dentist, Private Practice, Curitiba, Paraná, Brazil.
Jazyk:	angličtina
Zdroj:	The journal of contemporary dental practice [J Contemp Dent Pract] 2014 Nov 01; Vol. 15 (6), pp. 788-91. Date of Electronic Publication: 2014 Nov 01.
DOI:	10.5005/jp-journals-10024-1619
Abstrakt:	Aim: This paper describes a clinical case of a male with hypohidrotic ectodermal dysplasia submitted to rehabilitation and occlusal dental interventions with follow-up from 3 to 14 years of age. Background: Due to the severe effects on function and esthetics, the clinical manifestations of ectodermal dysplasia exert a negative impact on quality of life. However, oral rehabilitation in childhood poses a challenge due to growth and development. Case Description: A male with hypohidrotic ectodermal dysplasia began dental intervention at the age of 3 years. The clinical and radiographic exams revealed the absence of several primary and permanent teeth and abnormal shape of the primary maxillary incisors. The facial characteristics were compatible with hypohidrotic ectodermal dysplasia, such as a prominent brow, everted lips, fattened bridge of the nose and small vertical facial height. The treatment proposed involved rehabilitation through successive temporary partial dentures, functional orthopedics of the jaws, esthetic reconstruction of the anterior teeth, timely occlusal intervention and preventive actions for the control of dental caries and plaque. Conclusion: The present case demonstrates that early care plays a fundamental role in minimizing the biopsychosocial consequences of hypohidrotic ectodermal dysplasia and preparing the patient for future oral rehabilitation. Clinical Significance: Although, the literature offers a number of papers describing dental treatment for ectodermal dysplasia, few cases include long-term follow-up and the use of a functional orthopedic appliance in combination with removable dentures in such patients.
Databáze:	MEDLINE
Externí odkaz:	Zobrazit plný text záznamu