Management of the hemophilic pseudotumor of the abdomen: A rare pathological entity.

Autor: López-Gómez J; Instituto Mexicano Del Seguro Social, Department of General Surgery, Hospital de Especialidades Centro Médico Nacional La Raza, Seris y Zaachila SN, Col. La Raza, CP 02990 México, D.F., Mexico. Electronic address: javierlopgom@hotmail.com., Contreras JS; Instituto Mexicano Del Seguro Social, Department of General Surgery, Hospital de Especialidades Centro Médico Nacional La Raza, Seris y Zaachila SN, Col. La Raza, CP 02990 México, D.F., Mexico., Figueroa-Ruiz M; Instituto Mexicano Del Seguro Social, Department of General Surgery, Hospital de Especialidades Centro Médico Nacional La Raza, Seris y Zaachila SN, Col. La Raza, CP 02990 México, D.F., Mexico., Servín-Torres E; Instituto Mexicano Del Seguro Social, Department of General Surgery, Hospital de Especialidades Centro Médico Nacional La Raza, Seris y Zaachila SN, Col. La Raza, CP 02990 México, D.F., Mexico., Velázquez-García J; Instituto Mexicano Del Seguro Social, Department of General Surgery, Hospital de Especialidades Centro Médico Nacional La Raza, Seris y Zaachila SN, Col. La Raza, CP 02990 México, D.F., Mexico., Bevia-Pérez F; Instituto Mexicano Del Seguro Social, Department of General Surgery, Hospital de Especialidades Centro Médico Nacional La Raza, Seris y Zaachila SN, Col. La Raza, CP 02990 México, D.F., Mexico., Delgadillo-Teyer G; Instituto Mexicano Del Seguro Social, Department of General Surgery, Hospital de Especialidades Centro Médico Nacional La Raza, Seris y Zaachila SN, Col. La Raza, CP 02990 México, D.F., Mexico.
Jazyk: angličtina
Zdroj: International journal of surgery case reports [Int J Surg Case Rep] 2014; Vol. 5 (11), pp. 789-92. Date of Electronic Publication: 2014 Aug 30.
DOI: 10.1016/j.ijscr.2014.08.022
Abstrakt: Introduction: Hemophilic pseudotumor is a rare complication that occurs in patients with severe hemophilia. Results from multiple episodes of bleeding into the bones and soft tissues.
Presentation of Case: A 31 years old male patient, with severe hemophilia A. Diagnosed with an abdominal tumor 10 years ago during routine screening, that progressively grew to encompass the entire abdominal area, with symptoms of intestinal obstruction.
Discussion: Hemophilic pseudotumor appears as a painless tumor of slow growth that can compress vital organs producing bone destruction, muscle and skin necrosis. The tumor may have fistulas or break spontaneously.
Conclusion: The abdominal hemophilic pseudotumor is a rare pathological entity, with few reports worldwide, but must be considered in hemophilic patients with a well documented abdominal tumor.
(Copyright © 2014 The Authors. Published by Elsevier Ltd.. All rights reserved.)
Databáze: MEDLINE