| Autor: |
Meireles SI; Complexo Hospitalar Padre Bento de Guarulhos, Guarulhos, SP, Brazil., Andrade SM; Complexo Hospitalar Padre Bento de Guarulhos, Guarulhos, SP, Brazil., Gomes MF; Complexo Hospitalar Padre Bento de Guarulhos, Guarulhos, SP, Brazil., Castro FA; Complexo Hospitalar Padre Bento de Guarulhos, Guarulhos, SP, Brazil., Tebcherani AJ; Complexo Hospitalar Padre Bento de Guarulhos, Guarulhos, SP, Brazil. |
| Jazyk: |
angličtina |
| Zdroj: |
Anais brasileiros de dermatologia [An Bras Dermatol] 2014 Jul-Aug; Vol. 89 (4), pp. 679-80. |
| DOI: |
10.1590/abd1806-4841.20142646 |
| Abstrakt: |
Rendu-Osler-Weber Syndrome also known as Hereditary Hemorrhagic Telangiectasia is a rare systemic fibrovascular dysplasia, with dominant autosomal inheritance. It is characterized by recurrent epistaxis, mucocutaneous telangiectasia, visceral arteriovenous malformation and positive family history. There may be hematologic, neurologic, dermatologic and gastrointestinal complications. Therapy is supportive and aimed at preventing complications. In this article we report a case of Rendu-Osler-Weber in a 64 year-old man, with history of mucocutaneous telangiectasia since the third decade of life, recurrent epistaxis, positive family history and vascular ectasia in the gastrointestinal tract. |
| Databáze: |
MEDLINE |
| Externí odkaz: |
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